Neurofibromatosis Type 2

I was researching pathology about the Internal Auditory Canal when I found this-neurofibromatosis type 2. This is a genetic condition. The type 2 disorder is best diagnosed in 90% of patients with bilateral acoustic neuromas. This is a fast growing mass that usually also affects surrounding nerves. It can also cause lesions in the eye and dcan spread to the meninges and the spinal cord. Patients with this gene defect don't seem to have any symtoms until about middle age. Neurosurgery to removed to tumor from the IAC is just about the only treatment option. This will most likely result in hearing loss.